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一名早产孕妇产前发生的嗜铬细胞瘤相关性心肌病。

Pheochromocytoma-related cardiomyopathy during the antepartum period in a preterm pregnant woman.

作者信息

Nakajima Yoshiyuki, Masaoka Naoki, Sodeyama Masako, Tsuduki Yoko, Sakai Masato

机构信息

Department of Obstetrics and Gynecology, Tokyo Women's Medical University Yachiyo Medical Center, Chiba, Japan.

出版信息

J Obstet Gynaecol Res. 2011 Jul;37(7):908-11. doi: 10.1111/j.1447-0756.2010.01423.x. Epub 2011 Mar 9.

DOI:10.1111/j.1447-0756.2010.01423.x
PMID:21736670
Abstract

We report a rare case of pheochromocytoma-related cardiomyopathy during the preterm period. The patient was a 33-year-old woman who was referred to our hospital at 34 weeks' gestation. Her pulse was 130 beats/min, blood pressure of 186/90 mmHg and oxygen saturation was 30-40%. Fetal bradycardia prompted an emergency cesarean section and, nine minutes after admission, a boy weighing 2774 g was delivered with Apgar scores of 2 at 1 min and 5 at 5 min. A preoperative echocardiogram showed reduced fractional shortening of 19%. At 8 h after the operation, cardiac arrest developed. An intra-aortic balloon pump and percutaneous cardiopulmonary support were inserted, and continuous hemodiafiltration was also commenced, after which her cardiac function and respiratory function gradually improved. Urinary catecholamine levels were elevated and abdominal computerized tomography confirmed the presence of a right suprarenal mass. Four months after delivery, she underwent a laparoscopic adrenalectomy and the mass was found to be a pheochromocytoma.

摘要

我们报告了1例早产期间发生的嗜铬细胞瘤相关性心肌病罕见病例。患者为一名33岁女性,妊娠34周时转诊至我院。她的脉搏为130次/分钟,血压为186/90 mmHg,血氧饱和度为30% - 40%。胎儿心动过缓促使进行急诊剖宫产,入院9分钟后,一名体重2774 g的男婴出生,1分钟时阿氏评分2分,5分钟时为5分。术前超声心动图显示射血分数缩短率降低至19%。术后8小时,发生心脏骤停。插入主动脉内球囊泵和经皮心肺支持,并开始持续血液透析滤过,此后她的心脏功能和呼吸功能逐渐改善。尿儿茶酚胺水平升高,腹部计算机断层扫描证实右肾上腺有肿块。分娩后4个月,她接受了腹腔镜肾上腺切除术,发现肿块为嗜铬细胞瘤。

相似文献

1
Pheochromocytoma-related cardiomyopathy during the antepartum period in a preterm pregnant woman.一名早产孕妇产前发生的嗜铬细胞瘤相关性心肌病。
J Obstet Gynaecol Res. 2011 Jul;37(7):908-11. doi: 10.1111/j.1447-0756.2010.01423.x. Epub 2011 Mar 9.
2
Peripartum hypertension from pheochromocytoma: a rare and challenging entity.嗜铬细胞瘤所致围产期高血压:一种罕见且具有挑战性的病症。
Am J Hypertens. 2005 Oct;18(10):1306-12. doi: 10.1016/j.amjhyper.2005.04.021.
3
Hemodynamics associated with the diagnosis and treatment of pheochromocytoma in pregnancy.妊娠期嗜铬细胞瘤诊断与治疗的血流动力学
Am J Perinatol. 1992 Sep-Nov;9(5-6):464-6. doi: 10.1055/s-2007-999290.
4
Pheochromocytoma in pregnancy: a case report.妊娠期嗜铬细胞瘤:一例报告
J Med Assoc Thai. 1996 Apr;79(4):258-62.
5
Pheochromocytoma and pregnancy: a case report and review of anesthetic management.嗜铬细胞瘤与妊娠:一例病例报告及麻醉管理综述
Can J Anaesth. 2004 Feb;51(2):134-8. doi: 10.1007/BF03018772.
6
Bilateral pheochromocytoma during pregnancy.妊娠期双侧嗜铬细胞瘤
Arch Gynecol Obstet. 2005 Mar;271(3):276-9. doi: 10.1007/s00404-004-0654-6. Epub 2004 Jun 18.
7
Cesarean section at 28 weeks' gestation with resection of pheochromocytoma: perioperative antihypertensive management.妊娠28周时剖宫产并切除嗜铬细胞瘤:围手术期降压管理
J Clin Anesth. 2005 Jun;17(4):296-9. doi: 10.1016/j.jclinane.2004.07.006.
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Diagnosis and management of pheochromocytoma in pregnancy: a case report.妊娠期嗜铬细胞瘤的诊断与管理:一例病例报告
Am J Perinatol. 1998 Apr;15(4):259-62. doi: 10.1055/s-2007-993938.
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Hemodynamic observations during paroxysmal hypertension in a pregnancy with pheochromocytoma.嗜铬细胞瘤妊娠患者阵发性高血压期间的血流动力学观察。
Obstet Gynecol. 1989 Sep;74(3 Pt 2):439-41.
10
Recurrent pheochromocytoma during pregnancy.妊娠期复发性嗜铬细胞瘤
Obstet Gynecol. 1994 May;83(5 Pt 2):820-2.

引用本文的文献

1
Clinical characteristics and outcomes of pheochromocytoma crisis: a literature review of 200 cases.《200 例嗜铬细胞瘤危象的临床特征和转归:文献复习》
J Endocrinol Invest. 2022 Dec;45(12):2313-2328. doi: 10.1007/s40618-022-01868-6. Epub 2022 Jul 20.
2
Extracorporeal membrane oxygenation for pheochromocytoma-induced cardiogenic shock.体外膜肺氧合用于嗜铬细胞瘤诱发的心源性休克
Ann Intensive Care. 2016 Dec;6(1):117. doi: 10.1186/s13613-016-0219-4. Epub 2016 Nov 28.