Department of Pediatrics, University of Cincinnati, Cincinnati, OH 45229, USA.
Proc Natl Acad Sci U S A. 2011 Jul 26;108(30):12331-6. doi: 10.1073/pnas.1104499108. Epub 2011 Jul 11.
Cardiac hypertrophy is an adaptive growth process that occurs in response to stress stimulation or injury wherein multiple signal transduction pathways are induced, culminating in transcription factor activation and the reprogramming of gene expression. GATA4 is a critical transcription factor in the heart that is known to induce/regulate the hypertrophic program, in part, by receiving signals from MAPKs. Here we generated knock-in mice in which a known MAPK phosphorylation site at serine 105 (S105) in Gata4 that augments activity was mutated to alanine. Homozygous Gata4-S105A mutant mice were viable as adults, although they showed a compromised stress response of the myocardium. For example, cardiac hypertrophy in response to phenylephrine agonist infusion for 2 wk was largely blunted in Gata4-S105A mice, as was the hypertrophic response to pressure overload at 1 and 2 wk of applied stimulation. Gata4-S105A mice were also more susceptible to heart failure and cardiac dilation after 2 wk of pressure overload. With respect to the upstream pathway, hearts from Gata4-S105A mice did not efficiently hypertrophy following direct ERK1/2 activation using an activated MEK1 transgene in vivo. Mechanistically, GATA4 mutant protein from these hearts failed to show enhanced DNA binding in response to hypertrophic stimulation. Moreover, hearts from Gata4-S105A mice had significant changes in the expression of hypertrophy-inducible, fetal, and remodeling-related genes.
心肌肥厚是一种适应性生长过程,发生在应激刺激或损伤时,其中多个信号转导途径被诱导,最终导致转录因子激活和基因表达的重编程。GATA4 是心脏中的一个关键转录因子,已知通过接收 MAPKs 的信号来诱导/调节肥厚程序。在这里,我们生成了敲入小鼠,其中 Gata4 中丝氨酸 105(S105)的已知 MAPK 磷酸化位点被突变为丙氨酸,该位点增强了活性。纯合 Gata4-S105A 突变小鼠作为成体是存活的,尽管它们的心肌应激反应受损。例如,Gata4-S105A 小鼠对 2 周苯肾上腺素激动剂输注的心脏肥厚反应大大减弱,对 1 周和 2 周施加刺激时的压力超负荷的肥厚反应也是如此。Gata4-S105A 小鼠在压力超负荷 2 周后也更容易发生心力衰竭和心脏扩张。就上游途径而言,在体内使用激活的 MEK1 转基因直接激活 ERK1/2 后,Gata4-S105A 小鼠的心脏没有有效地肥大。从机制上讲,这些心脏的 GATA4 突变蛋白在对肥厚刺激的反应中未能显示出增强的 DNA 结合。此外,Gata4-S105A 小鼠的心脏在肥厚诱导、胎儿和重塑相关基因的表达上有显著变化。