Division of Prenatal Medicine, Department of Gynecology and Obstetrics, University of Schleswig-Holstein, Ratzeburger Allee 160, Campus Luebeck, 23538 Luebeck, Germany.
Arch Gynecol Obstet. 2011 Dec;284(6):1417-21. doi: 10.1007/s00404-011-1975-x. Epub 2011 Jul 12.
We report on the rare case of prenatally detected Taussig-Bing anomaly complicated by a coarctation of the aorta and a singular coronary artery in an otherwise healthy boy. After initially successful arterial switch, a high-grade stenosis of the singular coronary artery leads to a severe biventricular heart failure 5 weeks after the procedure. Although immediate surgical intervention was carried out, the boy died due to already severely impaired myocardial function. This review discusses the perinatal management, typical diagnostic features, and frequent additional anomalies, as well as surgical strategies in complex Taussig-Bing anomaly.
我们报告了一例罕见的产前检测到的 Taussig-Bing 异常,该异常合并主动脉缩窄和单一冠状动脉,患儿在其他方面健康。在最初成功进行动脉切换后,单一冠状动脉的严重狭窄导致手术后 5 周出现严重的双心室心力衰竭。尽管立即进行了手术干预,但由于已经严重受损的心肌功能,男孩还是死亡了。本文讨论了复杂 Taussig-Bing 异常的围产期管理、典型的诊断特征和常见的附加异常以及手术策略。