Kamath Vasantha, Prabhakar B, Lachikarathman D
Department of Medicine, Bangalore Medical College and Research Institute, Bangalore, Karnataka.
J Assoc Physicians India. 2011 Feb;59:114-5.
Primary Sjogren's is a multisystem autoimmune disease which predominantly affects the exocrine glands. pSS may occasionally present in an atypical way which may defy correct diagnosis for a considerable period of time. Clinically important immune-mediated cytopenia (or a combination of cytopenias) may be the first manifestation of an occult SS and have only been rarely described with Sjogren's. This case exemplifies the atypical presentation of pSS and hence should be considered in the differential diagnosis of patients with unexplained cytopenias.
原发性干燥综合征是一种多系统自身免疫性疾病，主要累及外分泌腺。原发性干燥综合征可能偶尔以非典型方式出现，在相当长一段时间内可能难以正确诊断。具有临床意义的免疫介导性血细胞减少（或血细胞减少的组合）可能是隐匿性干燥综合征的首发表现，而在干燥综合征中仅有很少的描述。本病例例证了原发性干燥综合征的非典型表现，因此在不明原因血细胞减少患者的鉴别诊断中应予以考虑。
