一名6岁女童的口腔寻常型天疱疮。

Oral pemphigus vulgaris in a 6-year-old girl.

作者信息

Laskaris G, Stoufi E

机构信息

Department of Oral Medicine and Pathology, Dental School, University of Athens, Greece.

出版信息

Oral Surg Oral Med Oral Pathol. 1990 May;69(5):609-13. doi: 10.1016/0030-4220(90)90245-n.

DOI:10.1016/0030-4220(90)90245-n

PMID:2185451

Abstract

An extremely rare case of pemphigus vulgaris in a 6-year-old girl with prominent oral manifestations is presented. The disease was first noted at the age of 2 years, yet no diagnosis was made. Clinical, histopathologic, and immunologic criteria served to confirm the diagnosis. A review of the literature has revealed 22 well-documented cases of pemphigus vulgaris in children under the age of 17 years. It is concluded that although oral pemphigus vulgaris is rare in young persons, it must be included in the differential diagnosis in those cases that have a prolonged history of erosive or bullous lesions.

摘要

本文报告了一例极为罕见的寻常型天疱疮，患者为一名6岁女童，有明显的口腔表现。该病最初在2岁时被发现，但当时未作出诊断。通过临床、组织病理学和免疫学标准得以确诊。文献回顾显示，有22例17岁以下儿童寻常型天疱疮的详细记录病例。得出的结论是，虽然寻常型天疱疮在年轻人中罕见，但对于那些有长期糜烂或水疱性病变病史的病例，必须将其纳入鉴别诊断。