Mukund Amar, Gamanagatti Shivanand
Amar Mukund, Department of Radiology, Institute of Liver and Biliary Sciences, New Delhi 110029, India.
World J Radiol. 2011 Jul 28;3(7):169-77. doi: 10.4329/wjr.v3.i7.169.
Budd-Chiari syndrome (BCS) consists of a group of disorders with obstruction of hepatic venous outflow leading to increased hepatic sinusoidal pressure and portal hypertension. Clinically, two forms of disease (acute and chronic) are recognized. Mostly the patients present with ascites, hepatomegaly, and portal hypertension. In acute disease the liver is enlarged with thrombosed hepatic veins (HV) and ascites, whereas in the chronic form of the disease there may be membranous occlusion of HV and/or the inferior vena cava (IVC), or there may be short or long segment fibrotic constriction of HV or the suprahepatic IVC. Due to advances in radiological interventional techniques and hardware, there have been changes in the management protocol of BCS with surgery being offered to patients not suitable for radiological interventions or having acute liver failure requiring liver transplantation. The present article gives an insight into various imaging findings and interventional techniques employed in the management of BCS.
布加综合征(BCS)是一组因肝静脉流出道梗阻导致肝窦压力升高和门静脉高压的疾病。临床上,可分为两种类型(急性和慢性)。大多数患者表现为腹水、肝肿大和门静脉高压。急性布加综合征患者肝脏肿大,肝静脉血栓形成,伴有腹水;而慢性布加综合征患者肝静脉和/或下腔静脉可能出现膜性闭塞,或者肝静脉或肝上型下腔静脉可能出现短段或长段纤维化狭窄。由于放射介入技术和设备的进步,布加综合征的治疗方案发生了变化,对于不适合放射介入治疗或患有急性肝衰竭需要肝移植的患者,可提供手术治疗。本文深入探讨了布加综合征管理中使用的各种影像学表现和介入技术。