Arikawa K, Shimokawa S, Maruko M, Watanabe K, Watanabe S, Taira A, Minagoe S
Second Department of Surgery, Kagoshima University School of Medicine.
J Cardiovasc Surg (Torino). 1990 Mar-Apr;31(2):231-4.
In the majority of cases, total anomalous pulmonary venous drainage (TAPVD) results in death in infancy or early childhood, with very few cases surviving until adulthood. We report here the surgical correction of TAPVD in two adult patients, a 43-year-old male and 51-year-old female. The postoperative course was uneventful in the two patients, both of whom showed marked improvement of clinical features. The six other surgical corrections of TAPVD in patients over 40 years of age that have been reported in Japan are also reviewed. The favorable results in these cases were associated with the following common factors: 1) unobstructed forms with large drainage veins, 2) large interatrial communication, 3) normal pulmonary vascular resistance with normal or slightly elevated pulmonary artery pressure, 4) low grade, delayed cyanosis, and 5) the supracardiac type of TAPVD.
在大多数情况下，完全性肺静脉异位引流（TAPVD）会导致婴儿期或儿童早期死亡，极少有病例能存活至成年期。我们在此报告两例成年患者（一名43岁男性和一名51岁女性）的TAPVD手术矫正情况。两名患者术后病程平稳，临床特征均有显著改善。我们还回顾了日本报道的另外6例40岁以上患者的TAPVD手术矫正情况。这些病例取得良好结果与以下共同因素有关：1）引流静脉粗大的无梗阻型；2）较大的心房交通；3）肺血管阻力正常且肺动脉压正常或轻度升高；4）发绀程度轻、出现延迟；5）心上型TAPVD。
