Davidson A, Paul T, Luhmer I, Kallfelz H C
Medizinische Hochschule Hannover, Abt. Kinderheilkunde III.
Klin Padiatr. 1989 Mar-Apr;201(2):130-2. doi: 10.1055/s-2007-1025289.
A 20-days-old female newborn was referred to our hospital because of persistent respiratory distress and a mild central cyanosis. On echocardiography from the suprasternal notch all 4 pulmonary veins could be visualized entering a common chamber posterior to the left atrium. This chamber communicated with a left vertical vein which drained through a large innominate vein into the right superior vena cava. The diagnosis of supracardiac type of TAPVD was confirmed the following day by angiography. The child was successfully operated and the postoperative course was uneventful. Cardiac catheterization carries an increased risk in patients with TAPVD in case of pulmonary hypertension due to pulmonary-venous obstruction. In experienced centers echocardiography has become the definite diagnostic method with a high level of sensitivity and specificity in patients with atrial sitlus solitus, unifocal pulmonary venous connection, and no evidence of other major congenital cardiac defects. With continuously improving knowledge an increasing number of newborns will benefit from improved ability to perform surgical repair without prior cardiac catheterization.
一名20日龄女婴因持续性呼吸窘迫和轻度中心性发绀被转诊至我院。经胸骨上切迹超声心动图检查,可见所有4条肺静脉汇入左心房后方的一个共同腔室。该腔室与一条左垂直静脉相通,左垂直静脉经一条粗大的无名静脉引流至右上腔静脉。次日经血管造影确诊为心上型完全性肺静脉异位引流。患儿手术成功,术后恢复顺利。对于因肺静脉梗阻导致肺动脉高压的完全性肺静脉异位引流患者,心导管检查风险增加。在经验丰富的中心,超声心动图已成为明确的诊断方法,对心房正位、单灶性肺静脉连接且无其他主要先天性心脏缺陷证据的患者具有较高的敏感性和特异性。随着知识的不断进步,越来越多的新生儿将受益于无需先行心导管检查即可进行手术修复的能力提升。