Ohba Shinichi, Matsumoto Fumihiko, Fujimaki Mitsuhisa, Ito Shin, Yokoyama Junkichi, Ikeda Katsuhisa
Department of Otorhinolaryngology, Juntendo University School of Medicine, Tokyo, Japan.
Auris Nasus Larynx. 2012 Jun;39(3):326-8. doi: 10.1016/j.anl.2011.07.012. Epub 2011 Sep 1.
This report describes an exceedingly rare case of adult embryonal rhabdomyosarcoma arising in the head and neck, which was initially diagnosed as a primary unknown cancer.
The patient underwent a radical neck dissection with the total excision of the tumor, which was diagnosed as embryonal rhabdomyosarcoma.
The patient received intensive adjuvant chemotherapy, and is still alive with no signs of recurrence or metastasis.
This case report demonstrates not only the rarity of this neoplasm but the importance of the differential diagnosis for planning the therapeutic strategy.
本报告描述了一例极为罕见的发生于头颈部的成人胚胎性横纹肌肉瘤，该病例最初被诊断为原发性不明癌症。
患者接受了根治性颈清扫术及肿瘤全切术，术后诊断为胚胎性横纹肌肉瘤。
患者接受了强化辅助化疗，目前仍然存活，无复发或转移迹象。
本病例报告不仅证明了这种肿瘤的罕见性，还凸显了鉴别诊断对制定治疗策略的重要性。
