Gupta Shilpy, Tyagi Parimala
Department of Pedodontics and Preventive Dentistry, People's Dental Academy, Bhopal, Madhya Pradesh, India.
Indian J Dent Res. 2011 Mar-Apr;22(2):348-51. doi: 10.4103/0970-9290.84291.
Ectodermal dysplasia is characterized by the absence or defects of two or more ectodermally derived structures. Anodontia or hypodontia is the most striking dental manifestation. In severe hypodontia, there is lack of alveolar development with consequent protrusion and eversion of the lips. Patients with anhidrotic forms suffer from heat intolerance due to lack of sweat glands and mild infections may lead to death in infancy from hyperthermia. A case of a 4-year-old child with anhidrotic ectodermal dysplasia with partial anodontia is presented. Dental, oral, and physical features were taken into consideration in diagnosis and treatment planning for this patient. Clinical management consisted of removable partial prosthesis in maxillary arch and complete denture prosthesis in mandibular arch. The main aim of the treatment was to improve psychological development and to promote better functioning of the stomatognathic system.
外胚层发育不全的特征是两个或更多外胚层衍生结构的缺失或缺陷。无牙症或少牙症是最显著的牙齿表现。在严重少牙症中,牙槽骨发育不足,导致嘴唇突出和外翻。无汗型患者因缺乏汗腺而不耐热,轻度感染可能导致婴儿期因体温过高而死亡。本文介绍了一例4岁患有无汗型外胚层发育不全伴部分无牙症的儿童病例。在对该患者进行诊断和治疗规划时,考虑了牙齿、口腔和身体特征。临床管理包括上颌可摘局部义齿和下颌全口义齿修复。治疗的主要目的是改善心理发育,促进口颌系统更好地发挥功能。