Ladda R, Gangadhar Sa, Kasat Vo, Bhandari Aj
Department of Prosthodontics, Rural Dental College, Loni, Maharashtra, India.
Ann Med Health Sci Res. 2013 Apr;3(2):277-81. doi: 10.4103/2141-9248.113679.
Ectodermal dysplasias are rare hereditary disorders characterized by abnormal development of certain tissues and structures of ectodermal origin. The condition is important for dentists as it affects teeth resulting in hypodontia or anodontia and dentist plays an important role in rehabilitation of the patient. Affected young children with anodontia not only have difficulties in eating and speaking but can also feel that they look different from their contemporaries. Well-fitting and functioning prosthesis could be a great help during their schooling years as it will improve appearance and thus boost their self confidence. We report a case of hypohidrotic ectodermal dysplasia in an 8-year-old boy who exhibited anodontia and was successfully rehabilitated with conventional complete dentures in both maxillary and mandibular arches. The aim of the treatment was to improve psychological development apart from promoting better functioning of the stomatognathic system.
外胚层发育不全是一种罕见的遗传性疾病，其特征是外胚层起源的某些组织和结构发育异常。这种情况对牙医来说很重要，因为它会影响牙齿，导致牙齿发育不全或无牙症，而牙医在患者的康复中起着重要作用。患有无牙症的幼儿不仅在进食和说话方面有困难，还可能觉得自己与同龄人不同。合适且功能良好的假牙在他们的上学期间会有很大帮助，因为它会改善外观，从而增强他们的自信心。我们报告一例8岁男孩的少汗型外胚层发育不全病例，该男孩表现为无牙症，并通过上颌和下颌弓的传统全口义齿成功康复。治疗的目的除了促进口颌系统更好地发挥功能外，还在于改善心理发育。
