Kikuchi Kazuhiro, Abe Riichiro, Shinkuma Satoru, Hamasaka Erika, Natsuga Ken, Hata Hiroo, Tateishi Yasuki, Shibata Masahiko, Tomita Yuki, Abe Yukiko, Aoyagi Satoru, Mukai Makio, Shimizu Hiroshi
Department of Dermatology, Hokkaido University Graduate School of Medicine, Sapporo, Tokyo, Japan.
Case Rep Dermatol. 2011 May;3(2):181-5. doi: 10.1159/000331325. Epub 2011 Aug 26.
Infantile myofibromatosis is a rare fibrous tumor of infancy. The cutaneous solitary type has typically an excellent prognosis. However, histologically, it is important to rule out leiomyosarcoma, which has a poor prognosis. The low frequency of mitosis was definitive for a diagnosis of infantile myofibromatosis. We present a cutaneous solitary-type case of infantile myofibromatosis. Following incisional biopsy, the tumor remitted spontaneously.
婴儿肌纤维瘤病是一种罕见的婴儿期纤维性肿瘤。皮肤孤立型通常预后良好。然而,在组织学上,排除预后较差的平滑肌肉瘤很重要。有丝分裂频率低是婴儿肌纤维瘤病诊断的确切依据。我们报告一例皮肤孤立型婴儿肌纤维瘤病病例。切开活检后,肿瘤自行消退。