外侧眶底孤立性婴儿肌纤维瘤病表现为自发消退。

Solitary infantile myofibromatosis in the lateral orbit floor showing spontaneous regression.

作者信息

Tokano H, Ishikawa N, Kitamura K, Noguchi Y

机构信息

Department of Otolaryngology-Head and Neck Surgery, Tokyo Medical and Dental University, Tokyo, Japan.

出版信息

J Laryngol Otol. 2001 May;115(5):419-21. doi: 10.1258/0022215011907811.

DOI:10.1258/0022215011907811

PMID:11410140

Abstract

Infantile myofibromatosis is a rare benign tumour usually occurring early in infancy. We describe the case of a 10-year-old boy with solitary infantile myofibromatosis in the left lateral orbit floor which regressed spontaneously. Although our patient was older than previously reported cases and showed bony destruction confirmed by computed tomography (CT), this tumour was diagnosed as infantile myofibromatosis based on immunohistochemical findings. The tumour disappeared spontaneously six months after incisional biopsy, that also indicated this tumour was an infantile myofibromatosis.

摘要

婴儿肌纤维瘤病是一种罕见的良性肿瘤，通常在婴儿早期出现。我们描述了一名10岁男孩的病例，其左侧眶底有孤立性婴儿肌纤维瘤病，该肿瘤自发消退。尽管我们的患者比先前报道的病例年龄更大，且计算机断层扫描（CT）证实有骨质破坏，但根据免疫组化结果，该肿瘤被诊断为婴儿肌纤维瘤病。切开活检6个月后，肿瘤自发消失，这也表明该肿瘤为婴儿肌纤维瘤病。