Nair Anup P, Bettaswamy Guruprasad, Jaiswal Awdhesh K, Garg Pallav, Jaiswal Sushila, Behari Sanjay
Department of Neurosurgery, Sanjay Gandhi Post Graduate Institute of Medical Sciences, Lucknow, Uttar Pradesh, India.
J Pediatr Neurosci. 2011 Jan;6(1):36-9. doi: 10.4103/1817-1745.84405.
Ewing's sarcoma causing unilateral proptosis along with bifrontal extradural infiltration in a child is an unusual presentation. A female patient presented with features of painless proptosis of the left eye with visual deterioration. Her radiology revealed an infiltrating intraorbital, extraconal tumor with intracranial bifrontal extradural extension causing mass effect. Total excision of the intraorbital and intracranial part of the tumor along with postoperative chemo- and radiotherapy brought about a substantial relief. The clinicoradiological presentation and management of this rare entity are discussed.
尤文肉瘤导致儿童单侧眼球突出并伴有双侧额部硬膜外浸润是一种不寻常的表现。一名女性患者表现为左眼无痛性眼球突出并伴有视力下降。她的影像学检查显示眶内、肌锥外有浸润性肿瘤，并向颅内双侧额部硬膜外延伸，产生占位效应。肿瘤的眶内和颅内部分全切，术后进行化疗和放疗，病情得到了显著缓解。本文讨论了这种罕见疾病的临床影像学表现及治疗方法。
