Bhatoe H S, Deshpande G U
Department of Neurosurgery, Command Hospital(SC), Maharashtra, India.
Br J Neurosurg. 1998 Apr;12(2):165-9. doi: 10.1080/02688699845348.
Primary Ewing's sarcoma of the cranium is extremely rare, with only 17 cases reported so far. We describe a further case with involvement of the frontotemporal region and the orbit. The patient, an adult male, was admitted with headache and papilloedema, and later developed localised swelling and proptosis. He was treated with surgery, radiotherapy and chemotherapy, and was free from metastases during a follow-up of 14 months. The prognosis of Ewing's sarcoma is improving with radiotherapy and chemotherapy. Further cases are needed to study the biological behaviour of primary cranial Ewing's sarcoma.
原发性颅骨尤因肉瘤极为罕见，迄今为止仅有17例报道。我们在此描述另外1例累及额颞部和眼眶的病例。该患者为成年男性，因头痛和视乳头水肿入院，随后出现局部肿胀和眼球突出。他接受了手术、放疗和化疗，在14个月的随访期间无转移。随着放疗和化疗的应用，尤因肉瘤的预后正在改善。需要更多病例来研究原发性颅骨尤因肉瘤的生物学行为。
