[上腔静脉综合征的罕见病因：髓外浆细胞瘤]

[A rare cause of superior vena cava syndrome: extramedullary plasmocytoma].

作者信息

Vanquaethem H, Salles Y, Quinquenel M-L, Cuguillière A

机构信息

Service de pneumologie, hôpital d'instruction des armées Robert Picqué, 351 route de Toulouse, Villenave d'Ornon, France.

出版信息

Rev Pneumol Clin. 2011 Oct;67(5):325-8. doi: 10.1016/j.pneumo.2010.09.003. Epub 2011 Jan 17.

DOI:10.1016/j.pneumo.2010.09.003

PMID:22017955

Abstract

We report the case of a 79-year-old man for whom investigations of superior vena cava syndrome have revealed extramedullary plasmocytoma. Extramedullary plasmocytoma (EMP) is the less frequent form of plasma cell neoplasms. The mediastinal location of EMP is rare, and its compressive nature is exceptional. Another particular feature we observed is that the EMP was associated with an authentic kappa light chain multiple myeloma.

摘要

我们报告了一例79岁男性患者，其经上腔静脉综合征检查发现了髓外浆细胞瘤。髓外浆细胞瘤（EMP）是浆细胞肿瘤中较为少见的类型。EMP位于纵隔的情况罕见，且具有压迫性的更是罕见。我们观察到的另一个特殊特征是，该EMP与真性κ轻链多发性骨髓瘤相关。