Hospital S, Francisco Xavier-Centro Hospitalar de Lisboa Ocidental, Internal Medicine Department, Lisboa, Portugal.
BMC Cardiovasc Disord. 2011 Oct 21;11:64. doi: 10.1186/1471-2261-11-64.
Pulmonary artery aneurysms are a rare condition, frequently associated with pulmonary hypertension. However, the evolution and treatment of this pathology is still not clear.
The authors report a case of a 65-year old patient with pulmonary artery aneurysm associated with pulmonary arterial hypertension. Due to a positive vasoreactivity test, treatment with calcium channel blockers was started with near normalization of the right cardiac pressures. Nevertheless, after 20 months of treatment, the pulmonary artery aneurysm size remained unchanged with an associated severe pulmonary regurgitation and causing extrinsic compression of the main left coronary artery. Surgical correction was successfully performed.
This is the first case report of a pulmonary artery aneurysm described to be associated with vasoreactive pulmonary hypertension in a living patient. Although medical therapy for pulmonary hypertension was started, surgical correction of the aneurysm was executed in order to prevent its future complications.
肺动脉瘤是一种罕见的疾病，常与肺动脉高压有关。然而，这种病理学的演变和治疗仍不清楚。
作者报告了一例 65 岁的肺动脉瘤合并肺动脉高压患者。由于血管反应性测试阳性，开始使用钙通道阻滞剂治疗，右心压力几乎恢复正常。然而，治疗 20 个月后，肺动脉瘤大小仍未改变，伴有严重的肺动脉瓣反流，并导致左冠状动脉主干受压。手术矫正成功。
这是首例在活体患者中描述与反应性肺动脉高压相关的肺动脉瘤的病例报告。尽管开始了肺动脉高压的药物治疗，但为了防止其未来发生并发症，仍对动脉瘤进行了手术矫正。
