Fesslova Vlasta, Saracino Antonio, Nuri Halkawt, Pomé Giuseppe
Department of Pediatric Cardiosurgery, Center of Fetal Cardiology, Policlinico San Donato IRCCS, Milan, Italy.
Interact Cardiovasc Thorac Surg. 2012 Mar;14(3):330-2. doi: 10.1093/icvts/ivr096. Epub 2011 Dec 6.
Cor triatriatum dexter is a rare congenital anomaly, caused by the persistence of the right valve of the sinus venosus, which divides the right atrium into two chambers and its diagnosis is rather difficult, due to the features often mimicking Ebstein's anomaly. We describe a case followed from the foetal age for a relative right ventricular hypoplasia and suspicious pulmonary stenosis and diagnosed after birth to have cor triatriatum dexter with an obstructing membrane in the right atrium, needing surgical correction, done successfully.
右三房心是一种罕见的先天性异常，由静脉窦右瓣持续存在引起，该瓣膜将右心房分为两个腔室，由于其特征常与埃布斯坦畸形相似，故诊断相当困难。我们描述了一例从胎儿期就因相对右心室发育不全和可疑肺动脉狭窄而被跟踪观察的病例，出生后诊断为右三房心，右心房有阻塞性隔膜，需要进行手术矫正，手术成功完成。
