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右三房心:宫内及出生后的异常特征

Cor triatriatum dexter: unusual features in utero and after birth.

作者信息

Fesslova Vlasta, Saracino Antonio, Nuri Halkawt, Pomé Giuseppe

机构信息

Department of Pediatric Cardiosurgery, Center of Fetal Cardiology, Policlinico San Donato IRCCS, Milan, Italy.

出版信息

Interact Cardiovasc Thorac Surg. 2012 Mar;14(3):330-2. doi: 10.1093/icvts/ivr096. Epub 2011 Dec 6.

Abstract

Cor triatriatum dexter is a rare congenital anomaly, caused by the persistence of the right valve of the sinus venosus, which divides the right atrium into two chambers and its diagnosis is rather difficult, due to the features often mimicking Ebstein's anomaly. We describe a case followed from the foetal age for a relative right ventricular hypoplasia and suspicious pulmonary stenosis and diagnosed after birth to have cor triatriatum dexter with an obstructing membrane in the right atrium, needing surgical correction, done successfully.

摘要

右三房心是一种罕见的先天性异常,由静脉窦右瓣持续存在引起,该瓣膜将右心房分为两个腔室,由于其特征常与埃布斯坦畸形相似,故诊断相当困难。我们描述了一例从胎儿期就因相对右心室发育不全和可疑肺动脉狭窄而被跟踪观察的病例,出生后诊断为右三房心,右心房有阻塞性隔膜,需要进行手术矫正,手术成功完成。

相似文献

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Cor triatriatum dexter: unusual features in utero and after birth.右三房心:宫内及出生后的异常特征
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本文引用的文献

1
Cor triatriatum dexter masquerading as Ebstein's anomaly.
Cardiol Young. 2011 Jun;21(3):354-6. doi: 10.1017/S1047951111000023. Epub 2011 Feb 4.
2
Cor triatriatum dexter: a rare cause of neonatal cyanosis.右三房心:新生儿青紫的罕见病因。
Anesth Analg. 2010 Mar 1;110(3):716-8; discussion 718. doi: 10.1213/ANE.0b013e3181cb5835. Epub 2009 Dec 23.
7
Persistent right sinus venosus valve.永存右窦静脉瓣
Br Heart J. 1982 Feb;47(2):183-5. doi: 10.1136/hrt.47.2.183.

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