成人高免疫球蛋白E与反复感染综合征

The hyperimmunoglobulinaemia E and recurrent infections syndrome in an adult.

作者信息

L'Huillier J P, Thoreux P H, Delaval P, Desrues B, Le Gall E, Kernec J, Delambre J F

机构信息

Service de Pneumologie, Centre Hospitalier Régional et Universitaire, Rennes, France.

出版信息

Thorax. 1990 Sep;45(9):707-8. doi: 10.1136/thx.45.9.707.

DOI:10.1136/thx.45.9.707

PMID:2218977

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC462705/

Abstract

A 27 year old white woman with a history of chronic eczema and episodes of serious infection of the chest, skin, and bone presented with acute respiratory failure. She was found to have a spontaneous right pneumothorax and a pneumatocele in the left upper lobe. Despite a left upper lobectomy she was left with chronic respiratory failure, bullous lung disease, and bilateral bronchiectasis. The hyperimmunoglobulinaemia E and recurrent infections syndrome was diagnosed only in adult life.

摘要

一名27岁的白人女性，有慢性湿疹病史，曾出现胸部、皮肤和骨骼的严重感染，此次因急性呼吸衰竭就诊。检查发现她有自发性右侧气胸和左上叶肺气囊。尽管接受了左上叶切除术，但她仍患有慢性呼吸衰竭、大疱性肺病和双侧支气管扩张。高免疫球蛋白E和反复感染综合征直到成年才被诊断出来。