Department of Nuclear Medicine, S Orsola-Malpighi University Hospital, Bologna, Italy.
Clin Nucl Med. 2012 Feb;37(2):196-7. doi: 10.1097/RLU.0b013e31823e9d54.
A case of Erdheim-Chester disorder, a rare non-Langerhans' cell histiocytosis, was referred for restaging by F-18 FDG PET/CT more than 10 years after initial diagnosis. The patient presented diabetes insipidus, hypergondotropic hypogonadism, and osteosclerotic lesions. Previous bone scintigraphy documented pathognomonic long bones' involvement. Chronic steroid and hormone replacement therapy was administered, and the patient was asymptomatic. F-18 FDG PET/CT was useful for disease restaging at cardiac and soft tissues level.
一名 Erdheim-Chester 病患者，一种罕见的非朗格汉斯细胞组织细胞增生症，在最初诊断 10 多年后因 F-18 FDG PET/CT 分期复查而被转诊。该患者表现为尿崩症、促性腺激素性性腺功能减退症和骨硬化性病变。之前的骨闪烁显像证实了长骨的特征性受累。患者接受了慢性皮质类固醇和激素替代治疗，无症状。F-18 FDG PET/CT 对心脏和软组织水平的疾病分期复查很有用。
