Department of Medicine, University of Toledo Medical Center, 3000 Arlington Avenue, Toledo, OH 43614, USA.
Saudi J Gastroenterol. 2012 Jan-Feb;18(1):59-61. doi: 10.4103/1319-3767.91728.
Caroli's syndrome is characterized by bile duct ectasia in association with hepatic fibrosis. It is usually transmitted in an autosomal recessive fashion and has been well documented to be associated with autosomal recessive polycystic kidney disease and occasionally with autosomal dominant polycystic kidney disease. However, there has been only few case reports published with Caroli's syndrome diagnosed postrenal transplantation.
Caroli 综合征的特征是胆管扩张合并肝纤维化。该病通常以常染色体隐性方式遗传，已有充分文献记载其与常染色体隐性多囊肾病相关，偶尔也与常染色体显性多囊肾病相关。然而，在肾移植后诊断为 Caroli 综合征的病例报告仅有少数几例。
