Karimzadeh-Soureshjani Elaheh, Pourhasan Farab, Simab Pouria Ahmadi, Shojaei Sajjad, Mohammadian Yasaman
Department of Clinical Sciences Abadan University of Medical Sciences Abadan Iran.
Student Research Committee Abadan University of Medical Sciences Abadan Iran.
Clin Case Rep. 2025 May 30;13(6):e70555. doi: 10.1002/ccr3.70555. eCollection 2025 Jun.
Caroli syndrome is a rare but serious congenital disorder associated with portal hypertension and polycystic kidney disease. Early diagnosis via imaging, particularly MRCP, is crucial to prevent life-threatening complications such as cholangitis and biliary cirrhosis. Timely intervention and close monitoring can significantly improve patient outcomes.
卡罗里综合征是一种罕见但严重的先天性疾病,与门静脉高压和多囊肾病有关。通过影像学检查,尤其是磁共振胰胆管造影(MRCP)进行早期诊断,对于预防诸如胆管炎和胆汁性肝硬化等危及生命的并发症至关重要。及时干预和密切监测可显著改善患者的预后。