Torrelo A, Rivera M T, Mampaso F, España A, Marcèn R, Ortuño J, Ledo A
Hospital Ramòn y Cajal, Madrid, Spain.
Postgrad Med J. 1990 Sep;66(779):773-5. doi: 10.1136/pgmj.66.779.773.
A patient with mycosis fungoides developed a nephrotic syndrome. Renal biopsy revealed deposits of a highly organized fibrillar material which did not stain with the typical amyloid stains; this picture was consistent with the diagnosis of non-amyloidotic fibrillary glomerulopathy or immunotactoid glomerulopathy. We believe this is the first case reported of immunotactoid glomerulopathy associated with mycosis fungoides. Possible pathogenetic implications are discussed with reference to previous publications.
一名蕈样肉芽肿患者出现了肾病综合征。肾活检显示有高度有序的纤维状物质沉积,这些物质不能被典型的淀粉样蛋白染色剂染色;此表现符合非淀粉样纤维性肾小球病或免疫触须样肾小球病的诊断。我们认为这是首例报道的与蕈样肉芽肿相关的免疫触须样肾小球病。并参考既往文献讨论了可能的发病机制。