骨内硬纤维瘤病相关性脊髓内病变。
Erdheim-Chester disease associated with intramedullary spinal cord lesion.
机构信息
Department of Radiology, Wakayama Medical University, Wakayama, Japan.
出版信息
Br J Radiol. 2012 Mar;85(1011):e62-4. doi: 10.1259/bjr/65720693.
Abstract
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We present a case of a 56-year-old male with ECD. As time progressed, involvement of the orbital fossa, cranial convexity, spinal cord, brain stem, thyroid, lung, retroperitoneum, lower extremity bones and skin were found. Previously reported cases reveal the frequency of ECD with spinal cord involvement is rare. Although this was a presumed diagnosis based on other lesions, our case is the first in which both intramedullary and epidural masses are present.
摘要
厄尔-道伊姆-切斯特病（ECD）是一种罕见的非朗格汉斯细胞组织细胞增生症。我们报告了一例 56 岁男性 ECD 病例。随着时间的推移，发现眼眶窝、颅凸、脊髓、脑干、甲状腺、肺、腹膜后、下肢骨骼和皮肤受累。以前报道的病例表明 ECD 合并脊髓受累的频率很少见。尽管这是基于其他病变的推测诊断，但我们的病例是首例同时存在髓内和硬膜外肿块的病例。
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