Retina. 2012 Feb;32 Suppl 1:450-60. doi: 10.1097/iae.0b013e31823f9a59.
To review the frequency and nature of idiopathic macular telangiectasia and to classify the disorders based on new clinical and imaging observations.
A combined retrospective and prospective analysis of newly diagnosed patients seen over a period of 3 years. Patients were identified based on the Gass-Blodi classification and were studied with biomicroscopy, fluorescein angiography, and optical coherence tomography.
Ten patients associated with aneurysmal telangiectasia (Gass-Blodi group 1) and 26 patients with perifoveal telangiectasia (Gass-Blodi group 2) were recruited. None with occlusive telangiectasia (Gass-Blodi group 3) were identified. New observations based on clinical, fluorescein angiographic, and optical coherence tomographic findings were made.
Our series was similar to that in the Gass-Blodi study in terms of frequency. New observations in groups 1 and 2 have expanded our knowledge of the clinical spectrum of these disorders. A simplified classification termed idiopathic macular telangiectasia with 2 distinct types (type I, or aneurysmal telangiectasia, and type II, or perifoveal telangiectasia) was proposed to produce a better understanding of the entities and to enhance teaching and research. The third type, occlusive telangiectasia, has been omitted from our classification based on its rarity and presence of capillary nonperfusion rather than macular telangiectasia as the primary abnormality.
回顾特发性黄斑毛细血管扩张症的发病频率和性质，并根据新的临床和影像学观察对其进行分类。
对 3 年来新诊断的患者进行回顾性和前瞻性联合分析。根据 Gass-Blodi 分类确定患者，并通过生物显微镜、荧光素血管造影和光学相干断层扫描进行研究。
共招募了 10 例与动脉瘤性毛细血管扩张症（Gass-Blodi 第 1 组）相关和 26 例与中心凹旁毛细血管扩张症（Gass-Blodi 第 2 组）相关的患者。未发现闭塞性毛细血管扩张症（Gass-Blodi 第 3 组）患者。根据临床、荧光素血管造影和光学相干断层扫描的新发现进行了新的观察。
我们的系列与 Gass-Blodi 研究在频率方面相似。第 1 组和第 2 组的新观察结果扩展了我们对这些疾病临床谱的认识。提出了一种简化的分类，称为特发性黄斑毛细血管扩张症，有 2 种不同类型（I 型，即动脉瘤性毛细血管扩张症，和 II 型，即中心凹旁毛细血管扩张症），以更好地理解这些实体，并加强教学和研究。第三种类型，闭塞性毛细血管扩张症，已被排除在我们的分类之外，因为其罕见且存在毛细血管无灌注，而不是黄斑毛细血管扩张症作为主要异常。
