与马凡综合征相关的大型肺动脉瘤。
Large pulmonary artery aneurysm associated with Marfan syndrome.
作者信息
Ting Peter, Jugdutt Bodh I, Le Tan Ju
机构信息
National Heart Centre, Singapore;
出版信息
Int J Angiol. 2010 Spring;19(1):e48-50. doi: 10.1055/s-0031-1278365.
Abstract
Pulmonary artery aneurysms are rare, and published data on the subject are limited. The first case of Marfan syndrome associated with a large pulmonary artery aneurysm complicated by pulmonary artery thrombi and pulmonary hypertension is described. Serial echocardiograms showed progressive dilation of the aneurysm, which reached a massive size of 90 mm. Cardiac catheterization, pulmonary angiography and computed tomography angiography were used in the preoperative evaluation. The patient died suddenly while awaiting a decision for surgical intervention, thereby underscoring the need for aggressive management.
摘要
肺动脉瘤较为罕见，关于该主题的已发表数据有限。本文描述了首例与大型肺动脉瘤相关的马凡综合征，该动脉瘤并发肺动脉血栓和肺动脉高压。系列超声心动图显示动脉瘤逐渐扩张，最大直径达90毫米。术前评估采用了心导管检查、肺血管造影和计算机断层血管造影。患者在等待手术干预决策时突然死亡，这凸显了积极治疗的必要性。
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