Poon Man-Chiu, Card Robert
The Department of Medicine and The Southern Alberta Rare Blood and Bleeding Disorders Comprehensive Care Program, University of Calgary and Alberta Health Services, Calgary, Alberta, Canada.
Transfus Apher Sci. 2012 Jun;46(3):299-307. doi: 10.1016/j.transci.2012.03.020. Epub 2012 Apr 13.
Hemophilia is an X-linked bleeding disorder caused by a deficiency of factor VIII or IX activity. We will review the use of blood products, including plasma derived and recombinant coagulation factor concentrates (CFCs), and other hemostatic agents central to the management of bleeding, surgical procedures, prophylaxis and inhibitors. However, management of hemophilia is more than just giving CFCs. Attention to the physical and psychosocial health of persons with hemophilia to improve their quality of life must be the goal. These goals can best be met by comprehensive care hemophilia (bleeding disorders) clinics designed to provide clinical service and education to persons with hemophilia and their families, and to conduct research to improve hemophilia care.
血友病是一种由凝血因子 VIII 或 IX 活性缺乏引起的 X 连锁出血性疾病。我们将回顾血液制品的使用，包括血浆源性和重组凝血因子浓缩物（CFCs），以及其他对出血管理、外科手术、预防和抑制剂至关重要的止血剂。然而，血友病的管理不仅仅是给予 CFCs。关注血友病患者的身体和心理健康以提高他们的生活质量必须成为目标。通过旨在为血友病患者及其家庭提供临床服务和教育，并开展研究以改善血友病护理的综合护理血友病（出血性疾病）诊所，能够最好地实现这些目标。
