[原发性淋巴水肿相关的胸腔积液：一种罕见的组合。附病例报告]
[Pleural effusion associated with primary lymphedema: a rare combination. Apropos of a case].
作者信息
Casado Y, Uresandi F, Montes M T, Llorente J L, Sobradillo V
机构信息
Servicio de Neumología, Hospital de Cruces, Baracaldo, Vizcaya.
出版信息
Med Clin (Barc). 1990 Jun 23;95(4):141-2.
A case of exclusive association of pleural effusions and primary lymphedema, without ungual dystrophy is described. This isolated combination is an uncommon clinical condition with only 11 cases reported in the literature. The pathogenesis is characterized by aplasia-hypoplasia of the lymphatic vessels with consequent defective lymphatic drainage. We present a pleural effusion associated with a left lower extremity cellulitis, we argue about the differential diagnosis and treat the patient with thoracocentesis and aspiration with a favourable evolution without recidive.
本文描述了一例仅伴有胸腔积液和原发性淋巴水肿，而无指甲营养不良的病例。这种孤立的组合是一种罕见的临床病症，文献中仅报道了11例。其发病机制的特征是淋巴管发育不全-发育不良，导致淋巴引流缺陷。我们报告了一例伴有左下肢蜂窝织炎的胸腔积液病例，讨论了鉴别诊断，并对患者进行了胸腔穿刺抽液治疗，病情进展良好，未复发。
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