伴有硬脊膜内脊髓脂肪瘤的多灶性胚胎发育不良性神经上皮肿瘤：病例报告

White Richard D, Kanodia Avinash K, Sammler Esther M, Brunton John N, Heath Craig A

Department of Clinical Radiology, Ninewells Hospital and Medical School, NHS Tayside, Dundee DDI 9SY, UK.

Case Rep Radiol. 2011;2011:734171. doi: 10.1155/2011/734171. Epub 2011 Sep 7.

We report a case of temporal lobe epilepsy and incomplete Brown-Sequard syndrome of the thoracic cord. Computed tomography and magnetic resonance (MR) imaging showed multiple supratentorial masses with the classical radiological appearances of multifocal dysembryoplastic neuroepithelial tumour (DNET). Spinal MR imaging revealed intradural lipomas, not previously reported in association with multifocal DNET. Presentation and imaging findings are discussed along with classification and natural history of the tumour.

我们报告一例颞叶癫痫合并胸段脊髓不完全性布朗 - 色夸综合征。计算机断层扫描和磁共振成像显示幕上有多个肿块，具有多灶性胚胎发育不良性神经上皮肿瘤（DNET）的典型放射学表现。脊髓磁共振成像显示硬膜内脂肪瘤，此前未见与多灶性 DNET 相关的报道。本文讨论了该病例的临床表现、影像学表现以及肿瘤的分类和自然病程。