Mansour M, Lassabe G, Lorentz C, Dupuit F, Rauscher M
Service de Cardiologie, Centre Hospitalier, Belfort.
Ann Cardiol Angeiol (Paris). 1990 Feb;39(2):115-23.
On the basis of a literature review and the study of 18 cases, the authors examine annuloaortic ectasia, which involves dilatation of the fibrous ring of the heart at the aortic orifice, marked by aortic regurgitation and dystrophic aneurysm of the ascending aorta. The authors noted a predominantly muscular disorder (14 males, 4 females) often detected from an assessment of aortic regurgitation without clinical, radiologic or specific electrical features. The value of echocardiography and Doppler echocardiography is clearly apparent from the diagnosis of the disease, monitoring of progress, selection of patients for invasive pre-operative explorations and post-operative surveillance. The developing gravity of this disease is stressed, rapid repercussions in the left ventricle intervening more than complications due to ectasia itself. This indicates the urgency of complete replacement of the whole ascending aorta and of the aortic valve with reimplantation of coronary arteries as in the Bentall or Bentall-Cabrol surgical intervention, seven cases of which have been reported with satisfactory results.
在文献综述及对18例病例研究的基础上，作者对瓣环主动脉扩张症进行了研究，该病表现为主动脉口处心脏纤维环扩张，特征为主动脉反流及升主动脉营养不良性动脉瘤。作者指出这主要是一种肌肉疾病（14例男性，4例女性），常通过主动脉反流评估发现，无临床、放射学或特定电学特征。超声心动图和多普勒超声心动图在该病诊断、病情监测、选择患者进行侵入性术前检查及术后监测方面的价值显而易见。强调了该病发展的严重性，左心室的快速影响比扩张本身引起的并发症更为显著。这表明像Bentall或Bentall - Cabrol手术干预那样完全替换整个升主动脉和主动脉瓣并重新植入冠状动脉的紧迫性，已报道7例该手术取得了满意效果。
