肝结节：一例原发性骨髓纤维化病例。
Hepatic nodule: a case of primary myelofibrosis.
作者信息
Cardoso Filipe Sousa, Pires João Veríssimo, Miranda José Simão, Araújo João Mascarenhas
机构信息
Department of Medicine, Hospital Professor Doutor Fernando Fonseca, Amadora, Portugal.
出版信息
BMJ Case Rep. 2011 Aug 4;2011:bcr0520114220. doi: 10.1136/bcr.05.2011.4220.
Abstract
Primary myelofibrosis is one of the entities that may manifest with lesions of extramedullary haematopoiesis, especially in spleen and liver. The authors report a case of primary myelofibrosis presenting incidentally as an intrahepatic focal lesion of extramedullary haematopoiesis, a rare occurrence that highlights the challenge of hepatic nodule differential diagnosis, and allows reflection about the diagnostic criteria and prognostic factors of this myeloproliferative disease.
摘要
原发性骨髓纤维化是可能表现为髓外造血病变的疾病之一，尤其是在脾脏和肝脏。作者报告了一例原发性骨髓纤维化，偶然表现为肝内髓外造血的局灶性病变，这种罕见情况凸显了肝结节鉴别诊断的挑战，并引发了对这种骨髓增殖性疾病的诊断标准和预后因素的思考。
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