Rios Lívia Teresa Moreira, Araujo Júnior Edward, Nardozza Luciano Marcondes Machado, Nacaratto Daniela Cristina, Moron Antonio Fernandes, Martins Marília da Glória
Mother-Child Unit, Universitary Hospital, Federal University of Maranhão (UFMA), 65020-560 São Luiz, MA, Brazil.
Case Rep Med. 2012;2012:273526. doi: 10.1155/2012/273526. Epub 2012 May 29.
Conjoined twins are rare variants of monozygotic twins, which result from an incomplete division of the embryonic disk. Cephalothoracopagus is a rare twin pregnancy described as imperfect fusion of the head and chest, but separated columns, limbs, and pelvis. They occur with incidence rates that range from 1 per 50,000 to 1 per 100,000 births; however, the incidence of the cephalothoracopagus variety is 1 per 58 conjoined twins. In the case of identical and symmetric faces caused by the orientations of the 2 notochordal axes that are perfectly ventroventral, they are called janiceps disymmetros. We present a prenatal diagnosis of a typical case of cephalothoracopagus janiceps disymmetros and the diagnostic confirmation by image and pathology exams.
联体双胎是单卵双胎的罕见变体,由胚盘不完全分裂所致。头胸联胎是一种罕见的双胎妊娠,其特征为头部与胸部融合不全,但脊柱、四肢和骨盆分离。联体双胎的发生率为每50,000至100,000例出生中有1例;然而,头胸联胎类型的发生率为每58例联体双胎中有1例。如果两个脊索轴完全腹侧对腹侧的方向导致面部相同且对称,则称为双侧双头联体。我们报告一例典型的双侧双头头胸联胎的产前诊断,并通过影像学和病理学检查进行诊断确认。