Small S, Murthy V, Sridhar A V
Children's Hospital, Leicester Royal Infirmary, University Hospitals of Leicester NHS Trust, Leicester, UK.
BMJ Case Rep. 2011 Apr 13;2011:bcr0120113719. doi: 10.1136/bcr.01.2011.3719.
Pachydermodactyly is a rare and benign superficial dermal fibromatosis, characterised by asymptomatic soft tissue hypertrophy of the lateral and dorsal aspects of the proximal interphalangeal joints. The majority affected are males, with only a few reported female cases, and usually begins to develop around the age of puberty. Pachydermodactyly affects the second, middle and ring fingers of the hand symmetrically and bilaterally. The majority of reported cases demonstrate bilateral involvement of joints, only a small proportion report unilateral involvement. In this case report the authors review literature and discuss a case of pachydermodactyly presenting a unilateral swelling of the proximal interphalangeal joints of only the left hand in a right-handed young male.
厚皮性指端纤维瘤病是一种罕见的良性浅表性皮肤纤维瘤病，其特征是近端指间关节的外侧和背侧出现无症状的软组织肥大。受影响的大多数是男性，仅有少数女性病例报道，通常在青春期左右开始发病。厚皮性指端纤维瘤病对称且双侧累及手部的第二、中指和环指。大多数报道病例显示关节双侧受累，只有一小部分报道为单侧受累。在本病例报告中，作者回顾了文献并讨论了一例厚皮性指端纤维瘤病病例，该病例表现为一名右利手年轻男性仅左手近端指间关节出现单侧肿胀。
