Rancy Schneider K, Granstein Richard D, Bansal Manjula, Barley Christopher L, Fields Theodore R, Wolfe Scott W
Division of Hand and Upper Extremity Surgery, Hospital for Special Surgery, New York, NY.
Department of Dermatology, New York-Presbyterian Hospital, New York, NY; Department of Dermatology, Weill Medical College of Cornell University, New York, NY.
J Hand Surg Am. 2016 Aug;41(8):e243-6. doi: 10.1016/j.jhsa.2016.04.013. Epub 2016 May 13.
Pachydermodactyly (PDD) is a rare form of digital fibromatosis characterized by painless soft tissue swelling, primarily about the proximal interphalangeal joints. The skin at the metacarpophalangeal joints, the palm, and the dorsum of the hand may also be involved. Because swelling can occur over the proximal interphalangeal and metacarpophalangeal joints, PDD may be confused with juvenile inflammatory arthropathy and may even occur concurrently. We present the clinical and histopathologic findings of a case of PDD characterized by bilateral proximal phalangeal involvement of the index through little fingers.
厚皮性多指（趾）纤维瘤病（PDD）是一种罕见的指（趾）纤维瘤病，其特征为无痛性软组织肿胀，主要累及近端指间关节。掌指关节、手掌和手背皮肤也可能受累。由于近端指间关节和掌指关节均可出现肿胀，PDD可能会与青少年炎性关节炎相混淆，甚至可能同时发生。我们报告一例以双侧示指至小指近端指骨受累为特征的PDD的临床及组织病理学表现。
