Serraj M, Kamaoui I, El Marzguioui N, Amara B, El Biaze M, Tizniti S, Benjelloun M C
Service de Pneumologie, CHU Hassan II, BP 5552, 30006 Fès Sidi Brahim, Fès, Maroc.
Rev Pneumol Clin. 2012 Oct;68(5):290-4. doi: 10.1016/j.pneumo.2012.04.001. Epub 2012 Jul 2.
Sclerosing mediastinitis is a rare and benign disease, which can cause obstruction of mediastinal structures, this determines the clinical presentation and prognosis. The obstruction of pulmonary venous structures secondary to mediastinal fibrosis has been rarely reported, clinically it mimics mitral stenosis. We describe the clinical case of a young patient with idiopathic sclerosing mediastinitis. The radiologic exams found stenosis of the right pulmonary artery, the right bronchus and pulmonary veins. Through this observation, we discuss this rare entity that although benign, can also be deadly. We study the different etiologies, clinical and therapeutic possibilities.
硬化性纵隔炎是一种罕见的良性疾病,可导致纵隔结构梗阻,这决定了临床表现和预后。继发于纵隔纤维化的肺静脉结构梗阻鲜有报道,临床上它类似二尖瓣狭窄。我们描述了一名特发性硬化性纵隔炎年轻患者的临床病例。影像学检查发现右肺动脉、右支气管和肺静脉狭窄。通过该观察,我们探讨了这种罕见疾病,其虽为良性,但也可能致命。我们研究了不同的病因、临床及治疗可能性。