The Ronald O. Perelman Department of Dermatology, New York University School of Medicine, New York, NY 10016 , USA.
Oncol Rep. 2012 Nov;28(5):1851-8. doi: 10.3892/or.2012.1977. Epub 2012 Aug 22.
Persistent paraprotein production in plasma cells necessitates a highly developed rough endoplasmic reticulum (ER) that is unusually susceptible to perturbations in protein synthesis. This biology is believed to account for the exquisite sensitivity of multiple myeloma (MM) to the proteasomal inhibitor bortezomib (BTZ). Despite remarkable response rates to BTZ in MM, BTZ carries the potential for serious side-effects and development of resistance. We, therefore, sought to identify therapeutic combinations that effectively disrupt proteostasis in order to provide new potential treatments for MM. We found that sulforaphane, a dietary isothiocyanate found in cruciferous vegetables, inhibits TNFα-induced Iκβ proteasomal degradation in a manner similar to BTZ. Like BTZ, sulforaphane synergistically enhances the cytotoxicity of arsenic trioxide (ATO), an agent with clinical activity in MM. ATO and sulforaphane co-treatment augmented apoptotic induction as demonstrated by cleavage of caspase-3, -4 and PARP. The enhanced apoptotic response was dependent upon production of reactive oxygen species (ROS) as demonstrated by glutathione depletion and partial inhibition of the apoptotic cascade after pretreatment with the radical scavenger N-acetyl-cysteine (NAC). Combination treatment resulted in enhanced ER stress signaling and activation of the unfolded protein response (UPR), indicative of perturbation of proteostasis. Specifically, combination treatment caused elevated expression of the molecular chaperone HSP90 (heat shock protein 90) along with increased PERK (protein kinase RNA-like endoplasmic reticulum kinase) and eIF2α phosphorylation and XBP1 (X-box binding protein 1) splicing, key indicators of UPR activation. Moreover, increased splicing of XBP1 was apparent upon combination treatment compared to treatment with either agent alone. Sulforaphane in combination with ATO effectively disrupts protein homeostasis through ROS generation and induction of ER stress to culminate in inhibition of protein secretion and apoptotic induction in MM. Our results suggest that sulforaphane deserves further investigation in combination with ATO in the treatment of MM.
浆细胞中持续的异常免疫球蛋白产生需要高度发达的粗面内质网(ER),而这种内质网对蛋白质合成的干扰异常敏感。这种生物学特性被认为是多发性骨髓瘤(MM)对蛋白酶体抑制剂硼替佐米(BTZ)极其敏感的原因。尽管 BTZ 在 MM 中具有显著的反应率,但 BTZ 有产生严重副作用和耐药性的风险。因此,我们试图确定有效的治疗组合,以破坏蛋白质稳态,从而为 MM 提供新的潜在治疗方法。我们发现,存在于十字花科蔬菜中的膳食异硫氰酸盐——萝卜硫素(SFN),以类似于 BTZ 的方式抑制 TNFα诱导的 Iκβ蛋白酶体降解。与 BTZ 相似,SFN 与三氧化二砷(ATO)协同增强细胞毒性,ATO 是 MM 中具有临床活性的药物。ATO 和 SFN 联合治疗可增强细胞凋亡诱导,如 caspase-3、-4 和 PARP 的裂解所示。增强的凋亡反应依赖于活性氧(ROS)的产生,如谷胱甘肽耗竭和在用自由基清除剂 N-乙酰半胱氨酸(NAC)预处理后部分抑制凋亡级联反应所示。联合治疗导致内质网应激信号增强和未折叠蛋白反应(UPR)激活,表明蛋白质稳态受到干扰。具体而言,联合治疗导致分子伴侣 HSP90(热休克蛋白 90)的表达升高,同时 PERK(蛋白激酶 RNA 样内质网激酶)和 eIF2α 磷酸化以及 XBP1(X 盒结合蛋白 1)剪接增加,这是 UPR 激活的关键指标。此外,与单独使用任一药物相比,联合治疗时 XBP1 的剪接增加更为明显。SFN 与 ATO 联合有效地通过 ROS 生成和内质网应激诱导破坏蛋白质稳态,最终导致蛋白质分泌抑制和 MM 中的细胞凋亡诱导。我们的结果表明,萝卜硫素值得进一步研究,与 ATO 联合用于 MM 的治疗。