Department of General, Gastroenterological and Oncological Surgery, Medical University of Warsaw, Warsaw, Poland.
Radiol Oncol. 2011 Mar;45(1):59-63. doi: 10.2478/v10019-010-0051-7. Epub 2010 Nov 25.
Mesenteric fibromatosis or intra-abdominal desmoid tumour is a rare proliferative disease affecting the mesentery. It is a locally aggressive tumour that lacks metastatic potential, but the local recurrence is common. Mesenteric fibromatosis with the intestinal involvement can be easily confused with other primary gastrointestinal tumours, especially with that of the mesenchymal origin.
We report a case of a 44-year-old female who presented with an abdominal mass that radiologically and pathologically mimicked a gastrointestinal stromal tumour.
The diagnosis of mesenteric fibromatosis should always be considered in the case of mesenchymal tumours apparently originating from the bowel wall that diffusely infiltrate the mesentery.
肠系膜纤维瘤病或腹腔内硬纤维瘤是一种罕见的增生性疾病，影响肠系膜。它是一种局部侵袭性肿瘤，缺乏转移潜能，但局部复发很常见。累及肠道的肠系膜纤维瘤容易与其他原发性胃肠道肿瘤混淆，尤其是起源于间叶组织的肿瘤。
我们报告了一例 44 岁女性患者，其腹部肿块在影像学和病理学上类似于胃肠道间质瘤。
在明显起源于肠壁并弥漫浸润肠系膜的间叶性肿瘤中，应始终考虑肠系膜纤维瘤病的诊断。
