Takazawa Takanori, Ikeda Ken, Murata Kiyoko, Kawase Yuji, Hirayama Takehisa, Ohtsu Motoharu, Harada Hisanobu, Totani Takeshi, Sugiyama Kunio, Kawabe Kiyokazu, Kano Osamu, Iwasaki Yasuo
Department of Neurology, Toho University Omori Medical Center, Japan.
Intern Med. 2012;51(17):2433-7. doi: 10.2169/internalmedicine.51.7737. Epub 2012 Sep 1.
We herein report a 26-year-old man with Guillain-Barré Syndrome (GBS) coexisting facial nerve palsy (FP) and deafness. He developed deafness, facial weakness, and limb weakness and numbness. Neurological examination showed facial diplegia, bilateral hypoacusia, areflexia and sensorimotor deficits in the distal limbs. The nerve conduction study findings supported the diagnosis of the demyelinating polyneuropathy. An audiogram revealed sensorineural hearing loss of 40-50 dB. Auditory brainstem responses disclosed no elicitation of waves I to IV on both sides. Magnetic resonance imaging depicted abnormal enhancement in bilateral facial and acoustic nerves. Physicians should pay more attention to auditory dysfunction in GBS patients with FP.
我们在此报告一名26岁患有吉兰-巴雷综合征（GBS）并伴有面神经麻痹（FP）和耳聋的男性。他出现了耳聋、面部无力以及肢体无力和麻木症状。神经系统检查显示双侧面瘫、双侧听力减退、腱反射消失以及远端肢体感觉运动功能障碍。神经传导研究结果支持脱髓鞘性多发性神经病的诊断。听力图显示感音神经性听力损失40 - 50分贝。听觉脑干反应显示双侧均未引出I至IV波。磁共振成像显示双侧面神经和听神经有异常强化。医生应更多关注伴有FP的GBS患者的听觉功能障碍。
