Management of a challenging arteriovenous malformation of the scalp and orbit in a patient with polycystic kidney disease.

Arteriovenous malformations are notorious for their propensity to bleed, sometimes with fatal consequences. We describe an unusual case of a patient with polycystic kidney disease and with a large arteriovenous malformation involving the orbit and scalp who presented with multiple episodes of profuse bleeding from the upper eyelid and loss of vision in the corresponding eye.