Hekmatfar Somayeh, Jafari Karim, Meshki Raziyeh, Badakhsh Samaneh
Post-graduate Student, Department of Pediatric Dentistry, Faculty of Dentistry, Shiraz University of Medical Sciences, Shiraz, Iran.
J Dent Res Dent Clin Dent Prospects. 2012 Summer;6(3):108-12. doi: 10.5681/joddd.2012.023. Epub 2012 Sep 1.
Ectodermal dysplasia is a hereditary disorder associated with abnormal development of embryonic ectodermally-derived organs including teeth, nails, hair and sweat glands. Hypodontia of the primary and permanent dentition is the most com-mon oral finding. Therefore, affected patients need dental prosthetic treatments during their developmental years. This re-port presents two cases of children affected by ectodermal dysplasia with anodontia. Oral rehabilitation was accomplished with removable acrylic prostheses. Treatment had major impacts on self-esteem, masticatory function, speech and facial esthetic.
外胚层发育不全是一种遗传性疾病,与胚胎外胚层来源器官(包括牙齿、指甲、毛发和汗腺)的异常发育有关。乳牙列和恒牙列的缺牙是最常见的口腔表现。因此,受影响的患者在发育阶段需要进行牙修复治疗。本报告介绍了两例患有无牙症的外胚层发育不全儿童病例。通过可摘丙烯酸义齿完成了口腔修复。治疗对自尊、咀嚼功能、言语和面部美观有重大影响。