Department of Medicine, Surgical Pathology & Cytopathology Unit, University Hospital of Padua, 35100, Padua, Italy.
Brain Pathol. 2012 Nov;22(6):865-8. doi: 10.1111/j.1750-3639.2012.00639.x.
Pleomorphic xanthoastrocytoma (PXA) is a rare astrocytic tumor that usually occurs in the superficial cerebral hemispheres of children and young adult and has a favorable prognosis. We report a case of a 14-year-old girl with a recent history of sciatica and ataxic gait. Pre- and post-contrast brain and spinal MRI revealed the presence of multiple solid lesions with a cystic component in the cerebellum and the spinal cord with a concomitant massive leptomeningeal involvement Histological and immunohistochemical findings were concordant with a final diagnosis of WHO grade II PXA. Even the biological indolent PXAs' behavior, this is the third report in the literature of such an unusual multicentric PXA with leptomeningeal dissemination.
多形性黄色星形细胞瘤(PXA)是一种罕见的星形细胞瘤,通常发生在儿童和年轻成年人的大脑半球浅表部位,预后良好。我们报告了一例 14 岁女孩,近期有坐骨神经痛和共济失调步态。脑和脊髓 MRI 增强前后显示小脑和脊髓存在多个伴有囊变成分的实性病变,伴有大量软脑膜受累。组织学和免疫组织化学检查结果与最终诊断为 WHO 二级 PXA 一致。即使是生物学惰性的 PXAs 行为,这也是文献中第三次报道如此罕见的多中心 PXA 伴有软脑膜播散。