Ko T, Gatz M G, Reisz G R
Department of Medicine Truman Medical Center, Kansas City.
Am Rev Respir Dis. 1990 Mar;141(3):795-8. doi: 10.1164/ajrccm/141.3.795.
Congenital unilateral absence of a pulmonary artery (UAPA) is a rare anomaly that is generally diagnosed in childhood and frequently associated with other cardiovascular abnormalities. Two patients with unilateral absence of a pulmonary artery first diagnosed as adults are reported. Our two cases demonstrate that presentation of UAPA may range from an incidental finding to chronic, life-threatening symptoms. Because UAPA may require urgent intervention, physicians should be alerted to the possibility of this entity presenting later in life.
先天性单侧肺动脉缺如（UAPA）是一种罕见的异常情况，通常在儿童期被诊断出来，并且常常与其他心血管异常相关。本文报告了两名首次在成年期被诊断为单侧肺动脉缺如的患者。我们的两个病例表明，UAPA的表现范围可能从偶然发现到慢性、危及生命的症状。由于UAPA可能需要紧急干预，医生应警惕这种疾病在生命后期出现的可能性。
