Börcek Alp Özgün, Egemen Emrah, Güngör Günhan, Baykaner Mustafa Kemali
Division of Pediatric Neurosurgery, Gazi University Medical School, Beşevler, 06500 Ankara, Turkey.
Childs Nerv Syst. 2013 Jan;29(1):11-5. doi: 10.1007/s00381-012-1959-6. Epub 2012 Nov 6.
Intracranial aneurysms are very rare in children. Headache and nausea/vomiting are the most prominent clinical findings. The only effective treatment is obliteration of aneurysm by surgical or endovascular techniques. Interrupted aortic arch is also a rare, congenital cardiovascular malformation characterized by the lack of continuity between the ascending and descending thoracic aorta. Aortic interruption is an uncommon cause of intracranial aneurysm. The course of disease is lethal unless effective collateral flow develops. Long-term survival may be possible with surgical repair.
We report on a 17-year-old boy affected with interrupted aortic arch disease and associated multiple intracranial aneurysms. Both aneurysms clipped successfully. After patient had recovered, he referred to cardiovascular surgery for further treatment.
Surgical or endovascular obliteration remains the main therapy for intracranial aneurysms. Accompanying systemic diseases such as interrupted aortic arch challenge the management of both diseases.
颅内动脉瘤在儿童中非常罕见。头痛和恶心/呕吐是最突出的临床表现。唯一有效的治疗方法是通过手术或血管内技术闭塞动脉瘤。主动脉弓中断也是一种罕见的先天性心血管畸形,其特征是升主动脉和降主动脉之间缺乏连续性。主动脉中断是颅内动脉瘤的罕见病因。除非形成有效的侧支循环,否则疾病进程是致命的。手术修复可能实现长期存活。
我们报告一名17岁患有主动脉弓中断疾病并伴有多发颅内动脉瘤的男孩。两个动脉瘤均成功夹闭。患者康复后,转诊至心血管外科接受进一步治疗。
手术或血管内闭塞仍然是颅内动脉瘤的主要治疗方法。诸如主动脉弓中断等伴随的全身性疾病对两种疾病的治疗都构成挑战。