Ben Bouali A, Armand P, Barthe J P, Boyer J, Simard C, Joubaud F
Sem Hop. 1979;55(41-42):1935-40.
The authors report the observation of a primary intestinal lymphangiectasy diagnosed on a young girl sent for isolated edema of her inferior members, recently appeared. Clinical examination was normal. Biology found a low protein rate at 33 g/l and a low lymph rate : 183 L/mm3. Hepatic and renal records were normal. Test to marked albumin asserted the exsudative enteropathy with a fecal radio-activity of 3.6% (N 1%). Biopsy of the small intestines set out lymphangiectasies of the intestinal mucosa. Referring to this observation and to literature date, the authors realise a clinical and physiopathological analysis of Waldmann's disease or primary intestinal lymphangiectasy.
作者报告了一例原发性肠淋巴管扩张症的观察病例，该病例为一名年轻女孩，因近期出现下肢孤立性水肿前来就诊。临床检查正常。实验室检查发现蛋白率低至33g/l，淋巴细胞率低：183L/mm³。肝脏和肾脏检查正常。白蛋白标记试验证实为渗出性肠病，粪便放射性为3.6%（正常范围1%）。小肠活检显示肠黏膜淋巴管扩张。参考该病例及文献资料，作者对Waldmann病或原发性肠淋巴管扩张症进行了临床和病理生理分析。
