Allwyn Joshua S, Shetty Lathika, Pare V S, Sebastian Roopa
Department of Anatomy, KVG Medical College, Sullia, 574327 DK, Karnataka, India.
Surg Radiol Anat. 2013 Jul;35(5):443-7. doi: 10.1007/s00276-012-1046-4. Epub 2012 Nov 30.
Pectus carinatum or protrusion deformity of chest wall is less frequently occurring anterior chest wall deformity when compared to pectus excavatum. It may be classified as type 1 or chondro-gladiolar and type 2 or chondro-manubrial deformity. Other variations seen are symmetrical and asymmetrical pectus carinatum. Here we present two unique case reports, one with chondro-manubrial deformity (Currarino-Silverman syndrome) and other with asymmetrical pectus carinatum having bifid rib which are some of the rare variations seen in pectus carinatum found during Computerized tomographic examination. Currarino-Silverman syndrome is a type 2 pectus carinatum, a rare deformity with chondro-manubrial involvement and usually associated congenital heart diseases. Early fusion of sternal plates is one of the known theories in producing this deformity. On the other hand, asymmetrical pectus deformity are usually seen due to imbalance or abnormality in growth plates of costal cartilages leading to forked rib or bifid rib, which are accidently seen on radiological examination. To conclude, our reports would help in differential diagnosis from frequently occurring conditions affecting chest like chondro-gladiolar deformity, pectus excavatum, chest wall tumours, rib fractures and intra thoracic ribs.
鸡胸或胸壁突出畸形与漏斗胸相比,是一种较少见的前胸壁畸形。它可分为1型或软骨 - 剑突型以及2型或软骨 - 胸骨柄型畸形。其他可见的变异有对称性和不对称性鸡胸。在此我们展示两例独特的病例报告,一例为软骨 - 胸骨柄畸形(库拉里诺 - 西尔弗曼综合征),另一例为伴有分叉肋骨的不对称鸡胸,这些都是在计算机断层扫描检查中发现的鸡胸中一些罕见的变异情况。库拉里诺 - 西尔弗曼综合征是2型鸡胸,是一种罕见的畸形,累及软骨 - 胸骨柄,通常伴有先天性心脏病。胸骨板早期融合是产生这种畸形的已知理论之一。另一方面,不对称鸡胸畸形通常是由于肋软骨生长板的不平衡或异常导致分叉肋骨或肋骨裂,这在放射学检查中偶然发现。总之,我们的报告将有助于与影响胸部的常见病症如软骨 - 剑突畸形、漏斗胸、胸壁肿瘤、肋骨骨折和胸内肋骨进行鉴别诊断。