Oldhafer K J, Ringe B, Wittekind C, Pichlmayr R
Department of Surgery, Hannover Medical School, Federal Republic of Germany.
Surgery. 1990 Apr;107(4):471-4.
The Budd-Chiari syndrome (BCS) is caused by hepatic venous outflow obstruction, which often leads to death as a result of portal hypertension and liver failure. Therapeutic approaches vary widely from conventional medical therapy to liver transplantation. If and when a patient suffering with BCS needs surgery remains a matter of contention. However, it is well accepted that portacaval shunt surgery and orthotopic liver transplantation represent efficient surgical treatments of this condition. We report on a patient with an eventful course after BCS was diagnosed. After portacaval shunt surgery the patient had acute liver failure and had a successful orthotopic liver transplantation.
布加综合征（BCS）是由肝静脉流出道梗阻引起的，常因门静脉高压和肝衰竭导致死亡。治疗方法从传统药物治疗到肝移植差异很大。患有布加综合征的患者是否以及何时需要手术仍是一个有争议的问题。然而，门静脉腔静脉分流术和原位肝移植是这种疾病有效的外科治疗方法，这一点已得到广泛认可。我们报告了一名布加综合征诊断后病程复杂的患者。门静脉腔静脉分流术后，该患者出现急性肝衰竭，并成功进行了原位肝移植。
