Bautista-Gómez Esperanza, Morales-García Víctor, Galván Espinosa Honorio, Flores-Romero Ana Luisa, Vásquez Santiago Edmundo, Pizarro Osorno Noel
Hospital General Aurelio Valdivieso, Oaxaca de Juárez, Oax.
Ginecol Obstet Mex. 2012 Oct;80(10):663-7.
The Mayer-Rokitansky-Kuster-Hauser is a rare congenital anomaly characterized by lack of vaginal and uterine development variable and normal ovaries. It results from agenesis or hypoplasia Müller duct system. Cervicovaginal agenesis as part of the complex syndrome, is even rarer. We report two cases: adolescent patient with primary amenorrhea, cervicovaginal agenesis and chronic pelvic pain, and a 28-year-old patient with primary amenorrhea, congenital absence of uterus and vagina.
迈耶-罗基坦斯基-库斯特-豪泽综合征是一种罕见的先天性异常，其特征为阴道和子宫发育不全或发育异常，而卵巢正常。它是由苗勒管系统发育不全或发育不良引起的。作为该复杂综合征一部分的宫颈阴道发育不全更为罕见。我们报告两例病例：一例是患有原发性闭经、宫颈阴道发育不全和慢性盆腔疼痛的青春期患者，另一例是患有原发性闭经、先天性子宫和阴道缺失的28岁患者。
