Department of Radiology, Seoul National University Hospital, Seoul 110-744, Korea.
Korean J Radiol. 2013 Mar-Apr;14(2):233-9. doi: 10.3348/kjr.2013.14.2.233. Epub 2013 Feb 22.
To analyze magnetic resonance imaging (MRI) findings of Müllerian remnants in young females clinically suspected of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome in a primary amenorrhea workup.
Fifteen young females underwent multiplanar T2- and transverse T1-weighted MRI at either a 1.5T or 3.0T MR imager. Two gynecologic radiologists reached consensus decisions for the evaluation of Müllerian remnants, vagina, ovaries, and associated findings.
All cases had bilateral uterine buds in the pelvic cavity, with unilateral cavitation in two cases. The buds had an average long-axis diameter of 2.64 ± 0.65 cm. In all cases, bilateral buds were connected with fibrous band-like structures. In 13 cases, the band-like structures converged at the midline or a paramedian triangular soft tissue lying above the bladder dome. The lower one-third of the vagina was identified in 14 cases. Fourteen cases showed bilateral normal ovaries near the uterine buds. One unilateral pelvic kidney, one unilateral renal agenesis, one mild scoliosis, and three lumbar sacralization cases were found as associated findings.
Typical Müllerian remnants in MRKH syndrome consist of bilateral uterine buds connected by the fibrous band-like structures, which converge at the midline triangular soft tissue lying above the bladder dome.
分析在原发性闭经检查中，临床怀疑 Mayer-Rokitansky-Küster-Hauser（MRKH）综合征的年轻女性的磁共振成像（MRI）结果。
15 名年轻女性在 1.5T 或 3.0T 磁共振成像仪上进行多平面 T2 加权和横轴 T1 加权 MRI。两名妇科放射科医生对 Müllerian 残余物、阴道、卵巢和相关发现进行了评估。
所有病例均在盆腔内有双侧子宫芽，其中 2 例单侧有空腔。芽的平均长轴直径为 2.64±0.65cm。所有病例的双侧芽均与纤维带状结构相连。在 13 例中，带状结构在中线或膀胱穹窿上方的正中三角形软组织处汇聚。14 例可识别阴道的下 1/3 段。14 例病例在子宫芽附近显示双侧正常卵巢。发现 1 例单侧盆腔肾、1 例单侧肾缺如、1 例轻度脊柱侧凸和 3 例腰椎骶化病例作为相关发现。
MRKH 综合征中典型的 Müllerian 残余物由双侧子宫芽通过纤维带状结构连接而成，这些结构在中线上方膀胱穹窿处的正中三角形软组织处汇聚。
