Matsushima T, Fukui M, Fujii K, Fujiwara S, Nagata S, Kitamura K, Kuwabara Y
Department of Neurosurgery, Faculty of Medicine, Kyushu University, Fukuoka, Japan.
Surg Neurol. 1990 Apr;33(4):276-80. doi: 10.1016/0090-3019(90)90048-t.
Two pediatric cases of unilateral Moyamoya disease are reported. The clinical symptoms and the findings of electroencephalography, angiography, and positron emission tomography in these cases were quite the same as those in the cases with bilateral involvement, which is typical of this disease. In both cases angiography demonstrated unilateral occlusion not only of the internal carotid artery but also of the posterior cerebral artery together with so-called Moyamoya vessels on the same side. Although infectious diseases were mentioned in the patients' histories, no obvious basic diseases related to the cerebrovascular occlusion were detected. We consider that these cases with unilateral involvement suggest the presence of unilateral Moyamoya disease without progression onto the opposite side.
报告了两例小儿单侧烟雾病病例。这些病例的临床症状以及脑电图、血管造影和正电子发射断层扫描的结果与双侧受累病例的典型表现完全相同。在这两例病例中，血管造影均显示不仅颈内动脉单侧闭塞，而且大脑后动脉也单侧闭塞，同时同侧出现所谓的烟雾血管。尽管患者病史中提到了感染性疾病，但未检测到与脑血管闭塞相关的明显基础疾病。我们认为这些单侧受累病例提示存在单侧烟雾病且未进展至对侧。
