Chandramouleeswari K, Anita S, Shivali B
Associate Professor of Pathology, Chengelpet Medical, College, Consultant Pathologist, Lister Metropolis, Chennai, India.
J Clin Diagn Res. 2012 Nov;6(9):1552-4. doi: 10.7860/JCDR/2012/4151.2558.
Hepatic mesenchymal hamartoma (HMH) is a hamartomatous growth of the mesenchymal tissue in the liver, which is of an uncertain aetiology. It is a space-occupying lesion that can potentially compress the adjacent organs, resulting in various complications, which include death. Hepatic mesenchymal hamartoma is characterized by the variable proliferation of the myxomatous mesenchyme and the malformed bile ducts. The differential diagnosis includes other paediatric hepatic masses. The diagnosis is typically made during infancy, and a complete resection is invariably curative. Here, we are reporting a case of HMH in a one year old female child who presented with abdominal distension. A clinical diagnosis of malignancy was made, based on the symptoms and imaging studies and a final diagnosis was made only after a histopathological examination. The lesion was potentially benign, with very rare chances of recurrence. This case has been presented due to its rarity.
肝间叶性错构瘤(HMH)是肝脏间叶组织的错构瘤样生长,其病因尚不确定。它是一种占位性病变,可能压迫相邻器官,导致各种并发症,包括死亡。肝间叶性错构瘤的特征是黏液样间叶组织和畸形胆管的不同程度增生。鉴别诊断包括其他小儿肝脏肿块。诊断通常在婴儿期做出,完整切除总是可以治愈的。在此,我们报告一例1岁腹胀女童的肝间叶性错构瘤病例。根据症状和影像学检查做出了恶性肿瘤的临床诊断,仅在组织病理学检查后才做出最终诊断。该病变可能是良性的,复发几率非常低。由于其罕见性,特此报告此病例。